Advertisement
Diagnostic Dilemma| Volume 134, ISSUE 8, P980-982, August 2021

Download started.

Ok

A Case of Paraneoplastic Pemphigus with Follicular Dendritic Cell Sarcoma

Published:February 20, 2021DOI:https://doi.org/10.1016/j.amjmed.2021.01.028
      A 42-year-old female presented with an 8-week history of progressive generalized rash and mucocutaneous ulcers associated with 50-pound weight loss. She had no personal or family history of autoimmune disease. No recent illness or change in medications before the onset of her rash.
      To read this article in full you will need to make a payment

      Purchase one-time access:

      Academic & Personal: 24 hour online accessCorporate R&D Professionals: 24 hour online access
      One-time access price info
      • For academic or personal research use, select 'Academic and Personal'
      • For corporate R&D use, select 'Corporate R&D Professionals'

      Subscribe:

      Subscribe to The American Journal of Medicine
      Already a print subscriber? Claim online access
      Already an online subscriber? Sign in
      Institutional Access: Sign in to ScienceDirect

      References

        • Paolino G
        • Didona D
        • Magliulo G
        • et al.
        Paraneoplastic pemphigus: insight into the autoimmune pathogenesis, clinical features and therapy.
        Int J Mol Sci. 2017; 18: 2532https://doi.org/10.3390/ijms18122532
        • Kim JH
        • Kim SC
        Paraneoplastic pemphigus: paraneoplastic autoimmune disease of the skin and mucosa.
        Front Immunol. 2019; 10: 1259https://doi.org/10.3389/fimmu.2019.01259
        • Poot AM
        • Diercks GF
        • Kramer D
        • et al.
        Laboratory diagnosis of paraneoplastic pemphigus.
        Br J Dermatol. 2013; 169: 1016-1024https://doi.org/10.1111/bjd.12479
        • Frew JW
        • Murrell DF
        Current management strategies in paraneoplastic pemphigus (paraneoplastic autoimmune multiorgan syndrome).
        Dermatol Clin. 2011; 29: 607-612https://doi.org/10.1016/j.det.2011.06.016
        • Ito Y
        • Makita S
        • Maeshima AM
        • et al.
        Paraneoplastic pemphigus associated with b-cell chronic lymphocytic leukemia treated with ibrutinib and rituximab.
        Intern Med. 2018; 57: 2395-2398https://doi.org/10.2169/internalmedicine.0578-17